Prognosis of secondary pulmonary alveolar proteinosis

• The prognosis of pulmonary alveolar proteinosis secondary to myelodysplastic syndrome, which accounts for 60% of secondary alveolar proteinosis cases, is poor.
• As shown in the figure below, the two-year survival rate from diagnosis is 40%.
• The severity of myelodysplastic syndrome at the time of diagnosis is irrelevant.
• Cortico-steroids affect the prognosis of treatment. The prognosis of patients who receive cortico-steroids is worse than that in patients who are not treated.